Complete Uterine Septum with Duplicate Cervix, Longitudinal Vaginal Septum and Unilateral Vaginal Obstruction (Herlyn-Werner-Wunderlich Syndrome): A Case Report of a Mullerian Duct Anomaly

Document Type : Case Report

Authors

Department of Obstetrics and Gynecology,School of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran

Abstract

Introduction:Herlyn-Werner-Wunderlich Syndrome (HWWs) is a rare variant of Mullerian duct anomalies. It is associated with a wide range of gynecological and obstetric complications, such as urinary incontinence, urinary retention, endometriosis, pelvic infection, pelvic pain and infertility.
Case presentation: We conducted the present study to investigate and manage HWWs with pelvic pain. The surgery was performed on the operative room of Imam Reza Hospital in April 2018.
Conclusion: The reported case is related to Herlyn-Werner-Wunderlich Syndrome, a rare congenital Mullerian duct anomaly, which it is not included in the current classification system of the Mullerian abnormalities of the American Fertility Association and is based on the typical pattern of caudal evolution towards cranial.

Keywords

References

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